Hirschsprung’s Disease (HD) is a congenital disorder of the intestines.


Hirschsprung's Disease

Children with Hirschprung's Disease have severe constipation. They may have other symptoms including, vomiting, explosive foul-smelling diarrhea, poor appetite, poor growth, fever, and abdominal distention. 


All children with HD will require surgery to remove the portion of the rectum/colon that does not have ganglion cells. Some children will require a colostomy for a few months before their pull through surgery (corrective operation); others will have a pull through without a colostomy. Your pediatric surgeon will decide which procedure is best for your child.

Long-term Outcomes

Children with HD will be followed closely throughout childhood and adolescence, with some being followed into adulthood. Many children will have some degree of bowel dysfunction. At the Colorectal Center at Primary Children’s Hospital we address ongoing problems and coordinate care between specialists to manage your child’s needs. We provide a Bowel Management Program, where we work closely with you and your child to assess function and provide a way for your child to stay clean of stool and prevent accidents.